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Sweet food preference in amyotrophic lateral sclerosis
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An elderly female developed anarthria with prominent emotionality over an 18-month period before specialist neurological assessment. Although tongue electromyography was normal, her corticobulbar signs were consistent with amyotrophic lateral sclerosis (ALS), a pattern that, in the absence of functional impairment outside of speech and swallowing, is appropriately termed progressive bulbar palsy. Such patients, often elderly females, may remain ambulant and independent for many months, sometimes years, despite typically rapid anarthria.1 Electromyography may be insensitive to denervation, even when genioglossus is sampled, and this can contribute to diagnostic delay …
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