A 47-year-old woman with Kearns–Sayre syndrome (KSS) and an implanted pacemaker for complete heart block was admitted to the intensive care unit following a cardiac arrest due to ventricular tachycardia (torsade de pointes) in the setting of QT prolongation. Complete heart blocks and ventricular tachycardia are implicated as mechanisms of sudden deaths in KSS; such patients may require pacemaker implantation and implantation of an automatic implantable cardioverter–defibrillator.
Statistics from Altmetric.com
If you wish to reuse any or all of this article please use the link below which will take you to the Copyright Clearance Center’s RightsLink service. You will be able to get a quick price and instant permission to reuse the content in many different ways.
Competing interests None.
Patient consent Obtained.
Provenance and peer review Not commissioned, externally peer reviewed. This paper was reviewed by Patrick Chinnery, Newcastle-upon-Tyne, UK.
Read the full text or download the PDF:
Other content recommended for you
- Post-acute management of the acquired long QT syndrome
- NKX2-5 genetic mutation in a young woman with an atrial septal defect presenting with complete heart block: ICD or bradycardia pacemaker?
- Dilated cardiomyopathy with cardiogenic shock in a child with Kearns-Sayre syndrome
- Atrial and ventricular tachyarrhythmias in military personnel
- Primary ventricular tachycardia in paediatric population in a tertiary centre
- Takotsubo cardiomyopathy-related complete heart block and torsades de pointes
- Dofetilide-induced torsade de pointes in high-grade atrioventricular node dysfunction
- The humble electrocardiogram
- Overdrive pacing in a patient with incessant torsades de pointes
- Modern management of arrhythmias