Peripheral neuropathy is a common reason for referral to neurology. Chronic acquired demyelinating neuropathies are an important and varied group with overlapping presentations, and may have an immune-mediated cause. Their correct diagnosis is important as they respond to different treatments; timely intervention can prevent irreversible axonal degeneration. We present a case that highlights the approach to an adult presenting with a chronic demyelinating neuropathy.
- POEMS syndrome
- plasma cell dyscrasia
- castleman’s disease
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Contributors AG, VP and DC contributed to the concept and design of the article. AG, PSK, RKS and PN contributed to the data acquisition, drafting of the text and/or the figures. All authors contributed to critical review and final approval of the manuscript.
Competing interests None declared.
Patient consent Next of kin consent obtained.
Provenance and peer review Not commissioned; externally peer reviewed by Michael Lunn, London, UK.
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