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Susac’s syndrome: characteristic imaging
  1. Arunmozhimaran Elavarasi1,
  2. Ankita Kothari2
  1. 1 Department of Neurology, All India Institute of Medical Sciences, New Delhi, India
  2. 2 Department of Ophthalmology, St John's Medical College, Bangalore, Karnataka, India
  1. Correspondence to Dr Arunmozhimaran Elavarasi, Department of Neurology, All India Institute of Medical Sciences, New Delhi, India; arun_ela{at}

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Case report

A 54-year-old man had a 12 month history of weakness of both lower limbs with urge urinary incontinence, 6 month history of visual loss and hearing impairment and a 1 month history of cognitive dysfunction. He had no constitutional symptoms. On examination, his visual acuity was reduced to perception of light only in both eyes; funduscopy identified branch retinal artery occlusion (figure 1). He had spastic weakness and hyperreflexia in the lower limbs. Pure-tone audiometry suggested severe sensorineural hearing loss. MR scan of the brain showed characteristic features of Susac’s syndrome (figure 2). Following high-dose methylprednisolone pulses, intravenous immunoglobulin and rituximab, …

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  • Contributors AE conceived the report and was involved in diagnosis and management of the case and in writing the manuscript. AK was involved in diagnosis and in writing the manuscript.

  • Funding The authors have not declared a specific grant for this research from any funding agency in the public, commercial or not-for-profit sectors.

  • Competing interests None declared.

  • Provenance and peer review Not commissioned; externally reviewed by Alasdair Coles, Cambridge, UK.

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