RT Journal Article
SR Electronic
T1 Relapsing cerebral amyloid angiopathy-related inflammation: the wax and the wane
JF Practical Neurology
JO Pract Neurol
FD BMJ Publishing Group Ltd
SP practneurol-2017-001599
DO 10.1136/practneurol-2017-001599
A1 Sharfaraz Salam
A1 Mayooreshan Anandarajah
A1 Sarah Al-Bachari
A1 Piyali Pal
A1 Jonathan Sussman
A1 Hisham Hamdalla
YR 2017
UL http://pn.bmj.com/content/early/2017/06/24/practneurol-2017-001599.abstract
AB Cerebral amyloid angiopathy-related inflammation (CAA-I) is a rare variant of cerebral amyloid angiopathy (CAA). Its precise pathophysiology remains uncertain and we currently have limited evidence on which immunosuppressive agents are the most effective in its treatment. The disease course of CAA-I disorders can vary from an isolated clinical event to recurrent episodes. We present a case of biopsy-confirmed CAA-I that gives insight into its potential relapsing nature and the challenges of its long-term management.