Table 1

American College of Rheumatology Neuropsychiatric Systemic Lupus Erythematosus classification (1999)

Central nervous systemPeripheral nervous system
Aseptic meningitisAcute inflammatory demyelinating polyradiculopathy
Cerebrovascular diseaseAutonomic disorder
Demyelinating syndromeMononeuropathy (single/multiple)
HeadacheMyasthenia gravis
Movement disorder (chorea)*Cranial neuropathy
MyelopathyPlexopathy
Seizure disorder*Polyneuropathy
Acute confusional state*
Anxiety disorder
Cognitive dysfunction*
Mood disorder*
Psychosis*
  • *Presentations associated with diffuse neuropsychiatric lupus.