Table 2

Immunotherapy choices in inflammatory neuromuscular diseases

SteroidsIntravenous Ig/SCIgAZAMTXMMFCYCPLEX
GBSNo1NoNoNoNo1
CIDP112No333
MMNNo1NoNoNo2No
Vasculitic neuropathy1No23*1No
Polymyositis12223**
Dermatomyositis12223**
Myasthenia gravis1cr>m2 (m)3 (m)2 (m)*1
  • 1 indicates first-line response, 2 indicates second-line response and 3 indicates third-line response.

  • *May consider in individual cases.

  • AZA, azathioprine; CIDP, chronic inflammatory demyelinating polyneuropathy; cr, treatment of myasthenic crisis; CYC, cyclophosphamide; GBS, Guillain-BarrĂ© syndrome; m, maintenance treatment; MMF, mycophenolate mofetil; MMN, multifocal motor neuropathy; MTX, methotrexate; No, not recommended; PLEX, plasma exchange; SCIg, subcutaneous immunoglobulin.