Table 1

Clinical course in 809 patients from 10 studies

Study	No	Monophasic attack	Relapsing attacks	Relapse leading to progressive disease	Progressive from onset
(Year published)	No	Monophasic attack	Relapsing attacks	Relapse leading to progressive disease	Progressive from onset
Kidd et al (1999)37	35	23	12	4	0
Akman-Demir et al (1999)38	152	82	53	53	17
Siva et al (2001)40	107	47	34	6	27
Ideguchi et al (2010)49	53	27	11	6	9
Hirohata et al (2012)50	111	61	6	9	25
Houman et al (2013)51	49	41	?	?	8
Noel et al (2014)53	115	45	33	14	23
Yan et al (2019)55	42	17	?	?	24
Bolek et al (2020)57	47	30	13	?	4