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A difficult case
Torsade de pointes in Kearns–Sayre syndrome
  1. Stéphan Wilmin1,
  2. David De Bels1,
  3. Sebastien Knecht2,
  4. Philippe Gottignies1,
  5. Marie-Dominique Gazagnes3,
  6. Jacques Devriendt1
  1. 1Department of Intensive Care, Brugmann University Hospital, Brussels, Belgium
  2. 2Department of Cardiology, Brugmann University Hospital, Brussels, Belgium
  3. 3Department of Neurology, Brugmann University Hospital, Brussels, Belgium
  1. Correspondence to David De Bels, Intensive Care Unit, Brugmann University Hospital, Rue du Foyer Schaerbeekois, 36, 1030 Brussels, Belgium; david.debels{at}chu-brugmann.be

Abstract

A 47-year-old woman with Kearns–Sayre syndrome (KSS) and an implanted pacemaker for complete heart block was admitted to the intensive care unit following a cardiac arrest due to ventricular tachycardia (torsade de pointes) in the setting of QT prolongation. Complete heart blocks and ventricular tachycardia are implicated as mechanisms of sudden deaths in KSS; such patients may require pacemaker implantation and implantation of an automatic implantable cardioverter–defibrillator.

https://doi.org/10.1136/practneurol-2012-000256

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    Footnotes

    • Competing interests None.

    • Patient consent Obtained.

    • Provenance and peer review Not commissioned, externally peer reviewed. This paper was reviewed by Patrick Chinnery, Newcastle-upon-Tyne, UK.

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